Transcatheter embolization of a high-flow congenital intrahepatic arterial-portal venous malformation in an infant

William D. Routh, Frederick Keller, Walter S. Cain, Stuart A. Royal

Research output: Contribution to journalArticle

29 Citations (Scopus)

Abstract

An intrahepatic arterial-portal venous malformation (APVM) was diagnosed in a 4 1 2-month-old infant with portal hypertension. Visceral angiography showed a large saccular vascular space in the left hepatic lobe with a multiplicity of feeding arteries and drainage into the left portal vein. The lesion was successfully treated by transcatheter embolization following two unsuccessful surgical procedures. Two years later portal vein thrombosis with cavernous transformation was diagnosed, possibly a consequence of the high-flow arterial-portal shunt and its subsequent occlusion. Knowledge of the anatomic differences between this rare congenital APVM and the more commonly occurring arterial-portal fistula is crucial in planning effective transcatheter embolotherapy or surgery for these lesions.

Original languageEnglish (US)
Pages (from-to)511-514
Number of pages4
JournalJournal of Pediatric Surgery
Volume27
Issue number4
DOIs
StatePublished - 1992
Externally publishedYes

Fingerprint

Portal Vein
Therapeutic Embolization
Portal Hypertension
Fistula
Blood Vessels
Drainage
Angiography
Thrombosis
Arteries
Liver

Keywords

  • arteries, therapeutic blockade
  • Arteriovenous malformations, hepatic, fistula, hepatoportal

ASJC Scopus subject areas

  • Surgery

Cite this

Transcatheter embolization of a high-flow congenital intrahepatic arterial-portal venous malformation in an infant. / Routh, William D.; Keller, Frederick; Cain, Walter S.; Royal, Stuart A.

In: Journal of Pediatric Surgery, Vol. 27, No. 4, 1992, p. 511-514.

Research output: Contribution to journalArticle

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