Primary Glaucoma Associated with Iridotrabecular Dysgenesis and Ectropion Uveae

Joseph L. Dowling, Daniel Albert, Leonard B. Nelson, David S. Walton

Research output: Contribution to journalArticle

39 Citations (Scopus)

Abstract

We present nine patients with unilateral congenital ectropion uveae (hyperplasia of the iris pigment border), iris hypoplasia, characteristic gonioscopic findings, and glaucoma. A majority of these patients also demonstrated mild ptosis. In none of these patients were there any associated systemic abnormalities. The apparent ectropion uveae results from spread of the iris pigment epithelium beyond the iris ruff and onto the anterior surface of the iris. In two patients with this abnormality, histopathologic and electron microscopic findings are presented. All patients with congenital ectropion uveae should be carefully examined periodically to detect glaucoma.

Original languageEnglish (US)
Pages (from-to)912-921
Number of pages10
JournalOphthalmology
Volume92
Issue number7
DOIs
StatePublished - Jan 1 1985
Externally publishedYes

Fingerprint

Ectropion
Iris
Glaucoma
Hyperplasia
Epithelium
Electrons

Keywords

  • congenital hyperplasia of iris pigment border
  • dysgenesis of filtration angle
  • ectropion uveae
  • glaucoma
  • iris stromal hypoplasia
  • neural crest cells

ASJC Scopus subject areas

  • Ophthalmology

Cite this

Primary Glaucoma Associated with Iridotrabecular Dysgenesis and Ectropion Uveae. / Dowling, Joseph L.; Albert, Daniel; Nelson, Leonard B.; Walton, David S.

In: Ophthalmology, Vol. 92, No. 7, 01.01.1985, p. 912-921.

Research output: Contribution to journalArticle

Dowling, Joseph L. ; Albert, Daniel ; Nelson, Leonard B. ; Walton, David S. / Primary Glaucoma Associated with Iridotrabecular Dysgenesis and Ectropion Uveae. In: Ophthalmology. 1985 ; Vol. 92, No. 7. pp. 912-921.
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