Brugada syndrome, an autosomal dominant genetic disorder, is characterised by abnormal electrocardiogram findings and increased risk of ventricular tachyarrhythmias and sudden cardiac death. Our report describes the multi-disciplinary perioperative management of a 28-year-old patient presenting to the Duke Transplant Center with a familial sodium channel gene SCN51 mutation concerning Brugada syndrome. We discuss the preparatory work-up, medication review and appropriate post-surgical follow-up for patients undergoing liver transplant surgery with cardiac monitoring.
- Brugada syndrome
- Implantable Cardiac Defibrillator
- Non-alcoholic steatohepatisis
- Orthotopic liver transplantation
ASJC Scopus subject areas
- Anesthesiology and Pain Medicine