Moyamoya syndrome associated with alagille syndrome: Outcome after surgical revascularization

Lissa Baird, Edward R. Smith, Rebecca Ichord, David A. Piccoli, Timothy J. Bernard, Nancy B. Spinner, R. Michael Scott, Binita M. Kamath

Research output: Contribution to journalArticle

13 Citations (Scopus)

Abstract

Vasculopathy is well-described in Alagille syndrome (ALGS); however, few data exist regarding neurosurgical interventions. We report 5 children with ALGS with moyamoya who underwent revascularization surgery. Postsurgical complications included 1 stroke and 1 death from thalamic hemorrhage. Global function improved in survivors. Revascularization is reasonably safe in patients with ALGS and may improve neurologic outcomes.

Original languageEnglish (US)
Pages (from-to)470-473
Number of pages4
JournalJournal of Pediatrics
Volume166
Issue number2
DOIs
StatePublished - Feb 1 2015

Fingerprint

Alagille Syndrome
Moyamoya Disease
Nervous System
Survivors
Stroke
Hemorrhage

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Medicine(all)

Cite this

Baird, L., Smith, E. R., Ichord, R., Piccoli, D. A., Bernard, T. J., Spinner, N. B., ... Kamath, B. M. (2015). Moyamoya syndrome associated with alagille syndrome: Outcome after surgical revascularization. Journal of Pediatrics, 166(2), 470-473. https://doi.org/10.1016/j.jpeds.2014.10.067

Moyamoya syndrome associated with alagille syndrome : Outcome after surgical revascularization. / Baird, Lissa; Smith, Edward R.; Ichord, Rebecca; Piccoli, David A.; Bernard, Timothy J.; Spinner, Nancy B.; Scott, R. Michael; Kamath, Binita M.

In: Journal of Pediatrics, Vol. 166, No. 2, 01.02.2015, p. 470-473.

Research output: Contribution to journalArticle

Baird, L, Smith, ER, Ichord, R, Piccoli, DA, Bernard, TJ, Spinner, NB, Scott, RM & Kamath, BM 2015, 'Moyamoya syndrome associated with alagille syndrome: Outcome after surgical revascularization', Journal of Pediatrics, vol. 166, no. 2, pp. 470-473. https://doi.org/10.1016/j.jpeds.2014.10.067
Baird, Lissa ; Smith, Edward R. ; Ichord, Rebecca ; Piccoli, David A. ; Bernard, Timothy J. ; Spinner, Nancy B. ; Scott, R. Michael ; Kamath, Binita M. / Moyamoya syndrome associated with alagille syndrome : Outcome after surgical revascularization. In: Journal of Pediatrics. 2015 ; Vol. 166, No. 2. pp. 470-473.
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