Moyamoya syndrome associated with alagille syndrome: Outcome after surgical revascularization

Lissa C. Baird, Edward R. Smith, Rebecca Ichord, David A. Piccoli, Timothy J. Bernard, Nancy B. Spinner, R. Michael Scott, Binita M. Kamath

Research output: Contribution to journalArticlepeer-review

13 Scopus citations

Abstract

Vasculopathy is well-described in Alagille syndrome (ALGS); however, few data exist regarding neurosurgical interventions. We report 5 children with ALGS with moyamoya who underwent revascularization surgery. Postsurgical complications included 1 stroke and 1 death from thalamic hemorrhage. Global function improved in survivors. Revascularization is reasonably safe in patients with ALGS and may improve neurologic outcomes.

Original languageEnglish (US)
Pages (from-to)470-473
Number of pages4
JournalJournal of Pediatrics
Volume166
Issue number2
DOIs
StatePublished - Feb 1 2015

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

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