Moyamoya syndrome associated with alagille syndrome: Outcome after surgical revascularization

Lissa C. Baird; Edward R. Smith; Rebecca Ichord; David A. Piccoli; Timothy J. Bernard; Nancy B. Spinner; R. Michael Scott; Binita M. Kamath

doi:10.1016/j.jpeds.2014.10.067

Moyamoya syndrome associated with alagille syndrome: Outcome after surgical revascularization

Lissa C. Baird, Edward R. Smith, Rebecca Ichord, David A. Piccoli, Timothy J. Bernard, Nancy B. Spinner, R. Michael Scott, Binita M. Kamath

Research output: Contribution to journal › Article › peer-review

18 Scopus citations

Abstract

Vasculopathy is well-described in Alagille syndrome (ALGS); however, few data exist regarding neurosurgical interventions. We report 5 children with ALGS with moyamoya who underwent revascularization surgery. Postsurgical complications included 1 stroke and 1 death from thalamic hemorrhage. Global function improved in survivors. Revascularization is reasonably safe in patients with ALGS and may improve neurologic outcomes.

Original language	English (US)
Pages (from-to)	470-473
Number of pages	4
Journal	Journal of Pediatrics
Volume	166
Issue number	2
DOIs	https://doi.org/10.1016/j.jpeds.2014.10.067
State	Published - Feb 1 2015
Externally published	Yes

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health

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title = "Moyamoya syndrome associated with alagille syndrome: Outcome after surgical revascularization",

abstract = "Vasculopathy is well-described in Alagille syndrome (ALGS); however, few data exist regarding neurosurgical interventions. We report 5 children with ALGS with moyamoya who underwent revascularization surgery. Postsurgical complications included 1 stroke and 1 death from thalamic hemorrhage. Global function improved in survivors. Revascularization is reasonably safe in patients with ALGS and may improve neurologic outcomes.",

author = "Baird, {Lissa C.} and Smith, {Edward R.} and Rebecca Ichord and Piccoli, {David A.} and Bernard, {Timothy J.} and Spinner, {Nancy B.} and Scott, {R. Michael} and Kamath, {Binita M.}",

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T1 - Moyamoya syndrome associated with alagille syndrome

T2 - Outcome after surgical revascularization

AU - Baird, Lissa C.

AU - Smith, Edward R.

AU - Ichord, Rebecca

AU - Piccoli, David A.

AU - Bernard, Timothy J.

AU - Spinner, Nancy B.

AU - Scott, R. Michael

AU - Kamath, Binita M.

PY - 2015/2/1

Y1 - 2015/2/1

N2 - Vasculopathy is well-described in Alagille syndrome (ALGS); however, few data exist regarding neurosurgical interventions. We report 5 children with ALGS with moyamoya who underwent revascularization surgery. Postsurgical complications included 1 stroke and 1 death from thalamic hemorrhage. Global function improved in survivors. Revascularization is reasonably safe in patients with ALGS and may improve neurologic outcomes.

AB - Vasculopathy is well-described in Alagille syndrome (ALGS); however, few data exist regarding neurosurgical interventions. We report 5 children with ALGS with moyamoya who underwent revascularization surgery. Postsurgical complications included 1 stroke and 1 death from thalamic hemorrhage. Global function improved in survivors. Revascularization is reasonably safe in patients with ALGS and may improve neurologic outcomes.

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ER -

Moyamoya syndrome associated with alagille syndrome: Outcome after surgical revascularization

Abstract

ASJC Scopus subject areas

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