Dermatitis in treated maple syrup urine disease

S. E. Koch, S. Packman, T. K. Koch, M. L. Williams

Research output: Contribution to journalArticle

22 Citations (Scopus)

Abstract

Two children who had classic maple syrup urine disease developed an eruptive dermatitis when plasma isoleucine levels, leucine levels, or both fell below normal during periods of protein restriction. The dermatitis was resistant to topical corticosteroid therapy. Rapid resolution occurred after treatment with isoleucine and leucine dietary supplements.

Original languageEnglish (US)
Pages (from-to)289-292
Number of pages4
JournalJournal of the American Academy of Dermatology
Volume28
Issue number2 II
StatePublished - 1993

Fingerprint

Maple Syrup Urine Disease
Isoleucine
Dermatitis
Leucine
Period Circadian Proteins
Dietary Supplements
Adrenal Cortex Hormones
Therapeutics

ASJC Scopus subject areas

  • Dermatology

Cite this

Koch, S. E., Packman, S., Koch, T. K., & Williams, M. L. (1993). Dermatitis in treated maple syrup urine disease. Journal of the American Academy of Dermatology, 28(2 II), 289-292.

Dermatitis in treated maple syrup urine disease. / Koch, S. E.; Packman, S.; Koch, T. K.; Williams, M. L.

In: Journal of the American Academy of Dermatology, Vol. 28, No. 2 II, 1993, p. 289-292.

Research output: Contribution to journalArticle

Koch, SE, Packman, S, Koch, TK & Williams, ML 1993, 'Dermatitis in treated maple syrup urine disease', Journal of the American Academy of Dermatology, vol. 28, no. 2 II, pp. 289-292.
Koch SE, Packman S, Koch TK, Williams ML. Dermatitis in treated maple syrup urine disease. Journal of the American Academy of Dermatology. 1993;28(2 II):289-292.
Koch, S. E. ; Packman, S. ; Koch, T. K. ; Williams, M. L. / Dermatitis in treated maple syrup urine disease. In: Journal of the American Academy of Dermatology. 1993 ; Vol. 28, No. 2 II. pp. 289-292.
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