Dermatitis in treated maple syrup urine disease

Susan E. Koch; Seymour Packman; Thomas K. Koch; Mary L. Williams

doi:10.1016/0190-9622(93)70036-S

Dermatitis in treated maple syrup urine disease

Susan E. Koch, Seymour Packman, Thomas K. Koch, Mary L. Williams

Research output: Contribution to journal › Article › peer-review

28 Scopus citations

Abstract

Two children who had classic maple syrup urine disease developed an eruptive dermatitis when plasma isoleucine levels, leucine levels, or both fell below normal during periods of protein restriction. The dermatitis was resistant to topical corticosteroid therapy. Rapid resolution occurred after treatment with isoleucine and leucine dietary supplements.

Original language	English (US)
Pages (from-to)	289-292
Number of pages	4
Journal	Journal of the American Academy of Dermatology
Volume	28
Issue number	2
DOIs	https://doi.org/10.1016/0190-9622(93)70036-S
State	Published - 1993
Externally published	Yes

ASJC Scopus subject areas

Dermatology

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10.1016/0190-9622(93)70036-S

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title = "Dermatitis in treated maple syrup urine disease",

abstract = "Two children who had classic maple syrup urine disease developed an eruptive dermatitis when plasma isoleucine levels, leucine levels, or both fell below normal during periods of protein restriction. The dermatitis was resistant to topical corticosteroid therapy. Rapid resolution occurred after treatment with isoleucine and leucine dietary supplements.",

author = "Koch, {Susan E.} and Seymour Packman and Koch, {Thomas K.} and Williams, {Mary L.}",

year = "1993",

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AU - Packman, Seymour

AU - Koch, Thomas K.

AU - Williams, Mary L.

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AB - Two children who had classic maple syrup urine disease developed an eruptive dermatitis when plasma isoleucine levels, leucine levels, or both fell below normal during periods of protein restriction. The dermatitis was resistant to topical corticosteroid therapy. Rapid resolution occurred after treatment with isoleucine and leucine dietary supplements.

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AN - SCOPUS:0027510169

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JO - Journal of the American Academy of Dermatology

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Dermatitis in treated maple syrup urine disease

Abstract

ASJC Scopus subject areas

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