Dermatitis in treated maple syrup urine disease

Susan E. Koch, Seymour Packman, Thomas K. Koch, Mary L. Williams

Research output: Contribution to journalArticlepeer-review

23 Scopus citations


Two children who had classic maple syrup urine disease developed an eruptive dermatitis when plasma isoleucine levels, leucine levels, or both fell below normal during periods of protein restriction. The dermatitis was resistant to topical corticosteroid therapy. Rapid resolution occurred after treatment with isoleucine and leucine dietary supplements.

Original languageEnglish (US)
Pages (from-to)289-292
Number of pages4
JournalJournal of the American Academy of Dermatology
Issue number2
StatePublished - 1993
Externally publishedYes

ASJC Scopus subject areas

  • Dermatology


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