Vertically Fused Tracheal Cartilage: An Underrecognized Anomaly

Andrew F. Inglis, John Kokesh, Joseph Siebert, Mark A. Richardson

Research output: Contribution to journalArticle

21 Citations (Scopus)

Abstract

Anterior vertical fusion of the tracheal cartilages with normal pars membranacea is a rarely described tracheal anomaly. We report four cases of this anomaly, three associated with craniosynostosis syndromes and one with Goldenhar's syndrome. The anomaly was documented at postmortem examination in one case, both endoscopically and at tracheotomy in two cases, and endoscopically in one case. Documentation from gross postmortem photographs, photomicrographs, and intraoperative endoscopic photographs is presented so that the anatomical aspects of this anomaly can be thoroughly understood and recognized. All four newborn patients developed recurrent lower respiratory tract infections, reactive airway disease, and chronically retained secretions attributable to this anomaly. Neither tracheal stenosis nor stridor was encountered. In the three surviving patients, the infections grew less frequent and less severe in later childhood. These observations suggest that this tracheobronchial anomaly may be associated with a variety of craniofacial syndromes and may alter airflow dynamics in a way that predisposes to retained secretions and chronic pulmonary disease. (Arch Otolaryngol Head Neck Surg. 1992;118:436-438).

Original languageEnglish (US)
Pages (from-to)436-438
Number of pages3
JournalArchives of Otolaryngology - Head and Neck Surgery
Volume118
Issue number4
DOIs
StatePublished - 1992
Externally publishedYes

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Cartilage
Goldenhar Syndrome
Tracheal Stenosis
Craniosynostoses
Tracheotomy
Respiratory Sounds
Respiratory Tract Infections
Documentation
Lung Diseases
Autopsy
Chronic Disease
Head
Newborn Infant
Infection

ASJC Scopus subject areas

  • Otorhinolaryngology
  • Surgery

Cite this

Vertically Fused Tracheal Cartilage : An Underrecognized Anomaly. / Inglis, Andrew F.; Kokesh, John; Siebert, Joseph; Richardson, Mark A.

In: Archives of Otolaryngology - Head and Neck Surgery, Vol. 118, No. 4, 1992, p. 436-438.

Research output: Contribution to journalArticle

Inglis, Andrew F. ; Kokesh, John ; Siebert, Joseph ; Richardson, Mark A. / Vertically Fused Tracheal Cartilage : An Underrecognized Anomaly. In: Archives of Otolaryngology - Head and Neck Surgery. 1992 ; Vol. 118, No. 4. pp. 436-438.
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