Type v aplasia cutis congenita: Case report, review of the literature, and proposed treatment algorithm

Daniel Morrow, Robert Schelonka, Alfons Krol, Michael Davies, Anna Kuang

Research output: Contribution to journalArticle

6 Citations (Scopus)

Abstract

Aplasia cutis congenita (ACC) is the congenital absence of skin. There are a number of different classifications based on distribution and associated findings. Type V ACC is unique in that the lesions are typically symmetric and found primarily on the trunk but can also include the upper and lower extremities. Type V is associated with the loss of a monozygotic co-twin during the late first or early second trimester. Here we present an extensive case of type V ACC and a review of the literature, including a summary of treatment and outcomes. From the available literature, it appears that there is no benefit from early surgical intervention, and therefore we propose a treatment algorithm that starts with conservative management.

Original languageEnglish (US)
JournalPediatric Dermatology
Volume30
Issue number6
DOIs
StatePublished - Nov 2013

Fingerprint

Ectodermal Dysplasia
Monozygotic Twins
Second Pregnancy Trimester
Lower Extremity
Therapeutics
Skin

ASJC Scopus subject areas

  • Dermatology
  • Pediatrics, Perinatology, and Child Health

Cite this

Type v aplasia cutis congenita : Case report, review of the literature, and proposed treatment algorithm. / Morrow, Daniel; Schelonka, Robert; Krol, Alfons; Davies, Michael; Kuang, Anna.

In: Pediatric Dermatology, Vol. 30, No. 6, 11.2013.

Research output: Contribution to journalArticle

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