Retinitis Pigmentosa: A Symposium on Terminology and Methods of Examination

Michael F. Marmor, Gustavo Aguirre, Geoffrey Arden, Eliot Berson, David G. Birch, Joann A. Boughman, Ronald Carr, Gian E. Chatrian, Monte Del Monte, John Dowling, Jay Enoch, Gerald A. Fishman, Ann B. Fulton, Charles A. Garcia, Peter Gouras, John Heckenlively, Dan Ning Hu, Richard A. Lewis, Gunter Niemeyer, John A. ParkerIdo Perlman, Harris Ripps, Michael A. Sandberg, Irwin Siegel, Richard G. Weleber, Mitchell L. Wolf, Lezheng Wu, Rockefeller S.L. Young

Research output: Contribution to journalArticle

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Abstract

This report represents a summary of opinions expressed at a meeting of specialists interested in retinitis pigmentosa (RP) and allied diseases, at which an attempt was made to define some minimum guidelines for ocular evaluation of these disorders. The term RP would be reserved for a group of hereditary disorders that diffusely involve photoreceptor and pigment epithelial function, and should not be used when a secondary cause is suspected. RP may be classified by genetic type (single cases without known affected relatives should be termed isolated or simplex), by the topography of retinal involvement, and by the severity of disease (to identify subtypes with mild or localized disease). Patients should have at least one comprehensive examination that conforms to basic standards, preferable early in the course of the disease. The visual field examination should use both a small and a large test light. Electroretinographic testing should (1) use a full-field stimulus, and (2) routinely document three independent responses (cone, rod, and mixed conerod). Patients should be identifiable for future study or therapeutic trials. They should be counseled about the disease and followed regularly. No specific therapy exists at present for most of these diseases, but optical and night vision aids are available. Sunglasses for outdoor use are recommended until more is known about whether long-term exposure to bright sunlight alters the course of these diseases.

Original languageEnglish (US)
Pages (from-to)126-131
Number of pages6
JournalOphthalmology
Volume90
Issue number2
DOIs
StatePublished - Jan 1 1983

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Keywords

  • dystrophy
  • electroretinogram
  • retina
  • retinitis pigmentosa

ASJC Scopus subject areas

  • Ophthalmology

Cite this

Marmor, M. F., Aguirre, G., Arden, G., Berson, E., Birch, D. G., Boughman, J. A., Carr, R., Chatrian, G. E., Del Monte, M., Dowling, J., Enoch, J., Fishman, G. A., Fulton, A. B., Garcia, C. A., Gouras, P., Heckenlively, J., Hu, D. N., Lewis, R. A., Niemeyer, G., ... Young, R. S. L. (1983). Retinitis Pigmentosa: A Symposium on Terminology and Methods of Examination. Ophthalmology, 90(2), 126-131. https://doi.org/10.1016/S0161-6420(83)34587-5