Prenatally diagnosed autosomal recessive polycystic kidney disease: initial postnatal management.

M. Munding, Amira Al-Uzri, D. Gralnek, D. Riden

Research output: Contribution to journalArticle

11 Citations (Scopus)

Abstract

We report a case of autosomal recessive polycystic kidney disease (ARPKD). A presumptive diagnosis was made after a late-term prenatal ultrasound revealed hypoplastic lungs, massive polycystic kidneys, and oligohydramnios. A full-term baby girl was delivered vaginally. Respiratory distress required intubation. Twelve hours after birth, she underwent bilateral nephrectomy and peritoneal dialysis catheter placement. The average kidney size was 150 g and 9.25 cm. Pathologic examination confirmed ARPKD. Peritoneal dialysis was started on the third day of life. The baby had no gross neurologic deficit. At 6 months of age, she was growing well, and the mother was a candidate to be a living-related kidney donor.

Original languageEnglish (US)
Pages (from-to)1097
Number of pages1
JournalUrology
Volume54
Issue number6
StatePublished - Dec 1999
Externally publishedYes

Fingerprint

Autosomal Recessive Polycystic Kidney
Peritoneal Dialysis
Oligohydramnios
Kidney
Polycystic Kidney Diseases
Neurologic Manifestations
Nephrectomy
Intubation
Catheters
Mothers
Tissue Donors
Parturition
Lung

ASJC Scopus subject areas

  • Urology

Cite this

Prenatally diagnosed autosomal recessive polycystic kidney disease : initial postnatal management. / Munding, M.; Al-Uzri, Amira; Gralnek, D.; Riden, D.

In: Urology, Vol. 54, No. 6, 12.1999, p. 1097.

Research output: Contribution to journalArticle

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