Management challenges of a large upper extremity vascular malformation in a patient with capillary malformation-arteriovenous malformation syndrome

Michael J. Zobel, Willieford Moses, Ashley Walther, Donuta Nowicki, Lori Howell, Joseph Miller, Chadi Zeinati, Dean M. Anselmo

Research output: Contribution to journalArticlepeer-review

Abstract

We describe a 17-year-old boy with capillary malformation-arteriovenous malformation syndrome and a massive vascular malformation of the right chest wall, shoulder, and upper arm. Persistent growth of the malformation caused cutaneous ulcerations and recurrent massive bleeding episodes. We proceeded with a modified shoulder disarticulation preceded by ligation of the subclavian artery and innominate vein by median sternotomy. After a staged debulking resection of the residual chest wall arteriovenous malformation with rotational transverse rectus abdominis myocutaneous flap coverage, the patient was discharged home safely. This report demonstrates that a multidisciplinary approach is critical for management of life-threatening complications in capillary malformation-arteriovenous malformation patients.

Original languageEnglish (US)
Pages (from-to)781-784
Number of pages4
JournalJournal of Vascular Surgery: Venous and Lymphatic Disorders
Volume9
Issue number3
DOIs
StatePublished - May 2021
Externally publishedYes

Keywords

  • Arteriovenous malformation
  • CM-AVM syndrome
  • Embolization
  • Pediatric

ASJC Scopus subject areas

  • Surgery
  • Cardiology and Cardiovascular Medicine

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