Low-grade fibromyxoid sarcoma of the vulva: A case report

Amanda M. VanSandt, Joline Bronson, Catherine Leclair, Atiya Mansoor, Martha Goetsch

Research output: Contribution to journalArticlepeer-review

11 Scopus citations

Abstract

Objective. The study aimed to describe a case of lowgrade fibromyxoid sarcoma arising from the vulva and to discuss the diagnostic challenges, clinical management, and epidemiology of this rare malignancy. Case. A 36-year-old woman presented to 3 separate emergency departments with complaints of a painful and slowly enlarging vulvar mass. Eventual gynecologic referral resulted in excision of a 6-cm, noncystic vulvar mass. Pathological diagnosis revealed low-grade fibromyxoid sarcoma. Later, a right radical hemivulvectomy ensured adequate margins, and 2 years later, the patient is free of recurrent and metastatic disease. Conclusions. Low-grade fibromyxoid sarcoma is a rare malignancy that may present in the lower genital tract. Definitive diagnosis is essential because low-grade fibromyxoid sarcoma may metastasize many years after diagnosis, thereby requiring indefinite clinical surveillance. h

Original languageEnglish (US)
Pages (from-to)79-81
Number of pages3
JournalJournal of lower genital tract disease
Volume17
Issue number1
DOIs
StatePublished - Jan 2013

Keywords

  • Low-grade fibromyxoid sarcoma
  • Lower genital tract
  • Vulva

ASJC Scopus subject areas

  • Obstetrics and Gynecology

Fingerprint

Dive into the research topics of 'Low-grade fibromyxoid sarcoma of the vulva: A case report'. Together they form a unique fingerprint.

Cite this