Low-grade fibromyxoid sarcoma of the vulva

A case report

Amanda VanSandt, Joline Bronson, Catherine Leclair, Atiya Mansoor, Martha Goetsch

Research output: Contribution to journalArticle

6 Citations (Scopus)

Abstract

Objective. The study aimed to describe a case of lowgrade fibromyxoid sarcoma arising from the vulva and to discuss the diagnostic challenges, clinical management, and epidemiology of this rare malignancy. Case. A 36-year-old woman presented to 3 separate emergency departments with complaints of a painful and slowly enlarging vulvar mass. Eventual gynecologic referral resulted in excision of a 6-cm, noncystic vulvar mass. Pathological diagnosis revealed low-grade fibromyxoid sarcoma. Later, a right radical hemivulvectomy ensured adequate margins, and 2 years later, the patient is free of recurrent and metastatic disease. Conclusions. Low-grade fibromyxoid sarcoma is a rare malignancy that may present in the lower genital tract. Definitive diagnosis is essential because low-grade fibromyxoid sarcoma may metastasize many years after diagnosis, thereby requiring indefinite clinical surveillance. h

Original languageEnglish (US)
Pages (from-to)79-81
Number of pages3
JournalJournal of Lower Genital Tract Disease
Volume17
Issue number1
DOIs
StatePublished - Jan 2013

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Vulva
Sarcoma
Hospital Emergency Service
Neoplasms
Epidemiology
Referral and Consultation

Keywords

  • Low-grade fibromyxoid sarcoma
  • Lower genital tract
  • Vulva

ASJC Scopus subject areas

  • Obstetrics and Gynecology

Cite this

Low-grade fibromyxoid sarcoma of the vulva : A case report. / VanSandt, Amanda; Bronson, Joline; Leclair, Catherine; Mansoor, Atiya; Goetsch, Martha.

In: Journal of Lower Genital Tract Disease, Vol. 17, No. 1, 01.2013, p. 79-81.

Research output: Contribution to journalArticle

VanSandt, Amanda ; Bronson, Joline ; Leclair, Catherine ; Mansoor, Atiya ; Goetsch, Martha. / Low-grade fibromyxoid sarcoma of the vulva : A case report. In: Journal of Lower Genital Tract Disease. 2013 ; Vol. 17, No. 1. pp. 79-81.
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