Intraosseous malignant peripheral nerve sheath tumor in a patient with neurofibromatosis

David G. Terry, Donald Sauser, Melissa D. Gordon

Research output: Contribution to journalArticle

15 Citations (Scopus)

Abstract

Malignant peripheral nerve sheath tumors (MPNSTs) are uncommon sarcomas that almost always arise in soft tissue. They can develop in pre-existing neurofibromas or schwannomas, de novo from peripheral nerves, or following radiation therapy. Primary intraosseous MPNST is rare and has been reported most frequently in the mandible. Of the reported cases involving the long bones, none has been associated with neurofibromatosis type 1 (NF-1). We report a case of MPNST arising in the femur in a patient with NF-1.

Original languageEnglish (US)
Pages (from-to)346-349
Number of pages4
JournalSkeletal Radiology
Volume27
Issue number6
DOIs
StatePublished - Jun 1998

Fingerprint

Neurofibromatoses
Neurilemmoma
Neurofibromatosis 1
Neurofibroma
Mandible
Peripheral Nerves
Sarcoma
Femur
Radiotherapy
Bone and Bones

Keywords

  • Bone
  • Malignant peripheral nerve sheath tumor
  • Neurofibromatosis

ASJC Scopus subject areas

  • Radiology Nuclear Medicine and imaging
  • Radiological and Ultrasound Technology

Cite this

Intraosseous malignant peripheral nerve sheath tumor in a patient with neurofibromatosis. / Terry, David G.; Sauser, Donald; Gordon, Melissa D.

In: Skeletal Radiology, Vol. 27, No. 6, 06.1998, p. 346-349.

Research output: Contribution to journalArticle

Terry, David G. ; Sauser, Donald ; Gordon, Melissa D. / Intraosseous malignant peripheral nerve sheath tumor in a patient with neurofibromatosis. In: Skeletal Radiology. 1998 ; Vol. 27, No. 6. pp. 346-349.
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