Hypoplastic left heart syndrome associated with large omphalocele and hypoplastic left bronchus

Michael Hainstock, Dianna Bardo, Mary Rice, Stephen Langley

    Research output: Contribution to journalArticlepeer-review

    3 Scopus citations

    Abstract

    We present a patient with the combination of hypoplastic left heart syndrome (HLHS), large omphalocele, and hypoplastic left bronchus who underwent a modified Norwood procedure and was successfully discharged home. The child required tracheostomy with home ventilation and we elected to delay the primary repair of the omphalocele. To our knowledge, this is the first reported case with this combination of anomalies surviving till hospital discharge. Our experience demonstrates the potential viability of patients with concurrent HLHS, large abdominal wall defects, and airway anomalies and may additionally advocate for delayed repair of large omphaloceles in patients with complex congenital heart disease.

    Original languageEnglish (US)
    Pages (from-to)878-880
    Number of pages3
    JournalPediatric Cardiology
    Volume31
    Issue number6
    DOIs
    StatePublished - Aug 1 2010

    Keywords

    • Hypoplastic bronchus
    • Hypoplastic left heart syndrome
    • Omphalocele
    • Single ventricle

    ASJC Scopus subject areas

    • Pediatrics, Perinatology, and Child Health
    • Cardiology and Cardiovascular Medicine

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