Hypoplastic left heart syndrome associated with large omphalocele and hypoplastic left bronchus

Michael Hainstock, Dianna Bardo, Mary Rice, Stephen Langley

Research output: Contribution to journalArticlepeer-review

3 Scopus citations

Abstract

We present a patient with the combination of hypoplastic left heart syndrome (HLHS), large omphalocele, and hypoplastic left bronchus who underwent a modified Norwood procedure and was successfully discharged home. The child required tracheostomy with home ventilation and we elected to delay the primary repair of the omphalocele. To our knowledge, this is the first reported case with this combination of anomalies surviving till hospital discharge. Our experience demonstrates the potential viability of patients with concurrent HLHS, large abdominal wall defects, and airway anomalies and may additionally advocate for delayed repair of large omphaloceles in patients with complex congenital heart disease.

Original languageEnglish (US)
Pages (from-to)878-880
Number of pages3
JournalPediatric Cardiology
Volume31
Issue number6
DOIs
StatePublished - Aug 2010
Externally publishedYes

Keywords

  • Hypoplastic bronchus
  • Hypoplastic left heart syndrome
  • Omphalocele
  • Single ventricle

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Cardiology and Cardiovascular Medicine

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