Dentatorubro-pallidoluysian atrophy of the myoclonus epilepsy type with posterior column degeneration

Ronald Pfeiffer, R. D. McComb

Research output: Contribution to journalArticle

17 Scopus citations


Dentatorubro-pallidoluysian atrophy (DRPLA) has a variable clinical presentation but the pathology is routinely confined to cerebellifugal and pallidofugal systems. We present a case of DRPLA of the myoclonus epilepsy type in which prominent posterior column degeneration was added to the pathological picture. This case illustrates the concept that the neurodegenerative diseases can be a continuum of both clinical and pathological presentations.

Original languageEnglish (US)
Pages (from-to)134-138
Number of pages5
JournalMovement Disorders
Issue number2
Publication statusPublished - 1990
Externally publishedYes


ASJC Scopus subject areas

  • Clinical Neurology
  • Neuroscience(all)

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